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Allelic imbalance on chromosomes 13 and 17 and mutation analysis of BRCA1 and BRCA2 genes in monozygotic twins concordant for breast cancer

Allelic imbalance on chromosomes 13 and 17 and mutation analysis of BRCA1 and BRCA2 genes in monozygotic twins concordant for breast cancer
Allelic imbalance on chromosomes 13 and 17 and mutation analysis of BRCA1 and BRCA2 genes in monozygotic twins concordant for breast cancer
To study genetic changes associated with the development of breast cancer and the extent of its hereditary predisposition, paraffin-embedded tissue samples were obtained from monozygotic twin pairs concordant for breast cancer through the linked Swedish Twin and Cancer Registries. DNA samples extracted from the matched tumour and normal tissues of nine twin pairs were analysed for allelic imbalance using a series of microsatellite markers on chromosomes 13 and 17, containing loci with known tumour suppressor genes. Multiple losses of constitutional heterozygosity (LOH), consistent with a loss of large genomic region, the whole chromosome or chromosome arm, was found in at least three pairs of twins. One double mitotic crossover was identified in one tumour sample in a pair concordant for LOH at multiple loci on both chromosomes. Recombination breakpoints were mapped to regions delineated by D13S218 and D13S263, and D13S155 and D13S279, respectively. In general, no genetic effect of losing the same allele within a twin pair was found. However, for one marker at chromosome 13 (D13S328, between the BRCA2 and the RB-1 loci) and two markers on chromosome 17 (D17S786, distal to the p53 locus, and D17S855, an intragenic BRCA1 marker) the proportion of twin pairs with the same LOH was significantly higher than expected. These regions may reflect hereditary genomic changes in our sample set. In addition, tumour DNA samples from a subset of 12 twin pairs were analysed for BRCA1 and BRCA2 mutations using exon-by-exon single-strand conformation polymorphism analysis. Two unclassified BRCA2 variants, with a putative pathogenic effect, were identified, but no pathogenic alterations were found in the BRCA1 gene.
pair 13, female, monozygotic, chromosomes, chromosome mapping, diseases in twins, humans, neoplasm proteins, genes, non-u.s.gov't, binomial distribution, environmental, adult, arm, genetics, pair 17, breast cancer, loss of heterozygosity, dna mutational analysis, human, middle aged, brca1, protein, proteins, sweden, pathology, twins, transcription factors, dna, aged, mutation, cancer, breast neoplasms, research support, analysis, registries, brca2 protein
0143-3334
27-33
Forsti, Asta
c700979e-12e6-417d-842c-cad292c19371
Luo, Liping
355d705b-e95d-4aa7-8598-c4755fee6a4b
Vorechovsky, Igor
7245de2f-8c9b-4034-8935-9a451d9b682e
Soderberg, Magnus
f13b9a83-a03b-4d19-9607-ee8ce2e7d96a
Lichtenstein, Paul
1e1573e3-7442-4d1f-969f-17dc9b7edaa4
Hemminki, Kari
4ce7a3f5-a609-4efd-b87d-1e8d0f9fc191
Forsti, Asta
c700979e-12e6-417d-842c-cad292c19371
Luo, Liping
355d705b-e95d-4aa7-8598-c4755fee6a4b
Vorechovsky, Igor
7245de2f-8c9b-4034-8935-9a451d9b682e
Soderberg, Magnus
f13b9a83-a03b-4d19-9607-ee8ce2e7d96a
Lichtenstein, Paul
1e1573e3-7442-4d1f-969f-17dc9b7edaa4
Hemminki, Kari
4ce7a3f5-a609-4efd-b87d-1e8d0f9fc191

Forsti, Asta, Luo, Liping, Vorechovsky, Igor, Soderberg, Magnus, Lichtenstein, Paul and Hemminki, Kari (2001) Allelic imbalance on chromosomes 13 and 17 and mutation analysis of BRCA1 and BRCA2 genes in monozygotic twins concordant for breast cancer. Carcinogenesis, 22 (1), 27-33. (doi:10.1093/carcin/22.1.27).

Record type: Article

Abstract

To study genetic changes associated with the development of breast cancer and the extent of its hereditary predisposition, paraffin-embedded tissue samples were obtained from monozygotic twin pairs concordant for breast cancer through the linked Swedish Twin and Cancer Registries. DNA samples extracted from the matched tumour and normal tissues of nine twin pairs were analysed for allelic imbalance using a series of microsatellite markers on chromosomes 13 and 17, containing loci with known tumour suppressor genes. Multiple losses of constitutional heterozygosity (LOH), consistent with a loss of large genomic region, the whole chromosome or chromosome arm, was found in at least three pairs of twins. One double mitotic crossover was identified in one tumour sample in a pair concordant for LOH at multiple loci on both chromosomes. Recombination breakpoints were mapped to regions delineated by D13S218 and D13S263, and D13S155 and D13S279, respectively. In general, no genetic effect of losing the same allele within a twin pair was found. However, for one marker at chromosome 13 (D13S328, between the BRCA2 and the RB-1 loci) and two markers on chromosome 17 (D17S786, distal to the p53 locus, and D17S855, an intragenic BRCA1 marker) the proportion of twin pairs with the same LOH was significantly higher than expected. These regions may reflect hereditary genomic changes in our sample set. In addition, tumour DNA samples from a subset of 12 twin pairs were analysed for BRCA1 and BRCA2 mutations using exon-by-exon single-strand conformation polymorphism analysis. Two unclassified BRCA2 variants, with a putative pathogenic effect, were identified, but no pathogenic alterations were found in the BRCA1 gene.

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More information

Published date: January 2001
Keywords: pair 13, female, monozygotic, chromosomes, chromosome mapping, diseases in twins, humans, neoplasm proteins, genes, non-u.s.gov't, binomial distribution, environmental, adult, arm, genetics, pair 17, breast cancer, loss of heterozygosity, dna mutational analysis, human, middle aged, brca1, protein, proteins, sweden, pathology, twins, transcription factors, dna, aged, mutation, cancer, breast neoplasms, research support, analysis, registries, brca2 protein

Identifiers

Local EPrints ID: 24701
URI: http://eprints.soton.ac.uk/id/eprint/24701
ISSN: 0143-3334
PURE UUID: 2f5a9a8a-eb39-485b-a2f7-fac3b8e375a9
ORCID for Igor Vorechovsky: ORCID iD orcid.org/0000-0002-6740-6502

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Date deposited: 03 Apr 2006
Last modified: 16 Mar 2024 03:32

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Contributors

Author: Asta Forsti
Author: Liping Luo
Author: Magnus Soderberg
Author: Paul Lichtenstein
Author: Kari Hemminki

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