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Narrowing the critical region within 11q24-qter for hypoplastic left heart and identification of a candidate gene, JAM3, expressed during cardiogenesis

Narrowing the critical region within 11q24-qter for hypoplastic left heart and identification of a candidate gene, JAM3, expressed during cardiogenesis
Narrowing the critical region within 11q24-qter for hypoplastic left heart and identification of a candidate gene, JAM3, expressed during cardiogenesis
Hypoplastic left heart is a severe human congenital heart defect characterized by left ventricular hypoplasiawith aortic and mitral valve atresia. A genetic etiology is indicated by an association of the hypoplastic left heart phenotype with terminal 11q deletions that span approximately 20 Mb (distal to FRA11B in 11q23). Here we define the breakpoints in four patients with heart defects in association with distal 11q monosomy and refine the critical region to an approximately 9-Mb region distal to D11S1351. Within this critical region we have identified JAM3, a member of the junction adhesion molecule family, as a strong candidate gene for the cardiac phenotype on the basis that it is expressed during human cardiogenesis in the structures principally affected in hypoplastic left heart.
0888-7543
475 - 478
Phillips, H.M.
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Renforth, G.L.
231858a2-568f-45d7-8edf-7fdac67126a5
Spalluto, C.
6802ad50-bc38-404f-9a19-40916425183b
Hearn, T.
b4714fee-dc23-414f-afc6-11e7670ca8b3
Curtis, A.R.
e0299952-d903-4c55-b24f-8dd35df171d6
Craven, L.
f42b0d0b-6fc9-4259-a41c-b5b3d231ca35
Havarani, B.
ee395345-6cc2-4efb-8551-f8508a3e8d5d
Clement-Jones, M.
f9f9c0a9-8769-48e4-9157-915bcf9c39bb
English, C.
5352c2ad-4897-4e21-8745-1723c1209f70
Stumper, O.
95b29994-b829-403e-a3ab-1044f2b97aea
Salmon, T.
44e1ec1d-fb1a-441e-b6ca-4164bf5af509
Hutchinson, S.
b8916167-2f39-4738-b405-58f36b5dba45
Jackson, M.S.
fb309c89-0b3a-490e-b198-ac140fa5e34b
Wilson, D.I.
1500fca1-7082-4271-95f4-691f1d1252a2
Phillips, H.M.
8689e46a-9686-45fb-8e02-934465fa0336
Renforth, G.L.
231858a2-568f-45d7-8edf-7fdac67126a5
Spalluto, C.
6802ad50-bc38-404f-9a19-40916425183b
Hearn, T.
b4714fee-dc23-414f-afc6-11e7670ca8b3
Curtis, A.R.
e0299952-d903-4c55-b24f-8dd35df171d6
Craven, L.
f42b0d0b-6fc9-4259-a41c-b5b3d231ca35
Havarani, B.
ee395345-6cc2-4efb-8551-f8508a3e8d5d
Clement-Jones, M.
f9f9c0a9-8769-48e4-9157-915bcf9c39bb
English, C.
5352c2ad-4897-4e21-8745-1723c1209f70
Stumper, O.
95b29994-b829-403e-a3ab-1044f2b97aea
Salmon, T.
44e1ec1d-fb1a-441e-b6ca-4164bf5af509
Hutchinson, S.
b8916167-2f39-4738-b405-58f36b5dba45
Jackson, M.S.
fb309c89-0b3a-490e-b198-ac140fa5e34b
Wilson, D.I.
1500fca1-7082-4271-95f4-691f1d1252a2

Phillips, H.M., Renforth, G.L., Spalluto, C., Hearn, T., Curtis, A.R., Craven, L., Havarani, B., Clement-Jones, M., English, C., Stumper, O., Salmon, T., Hutchinson, S., Jackson, M.S. and Wilson, D.I. (2002) Narrowing the critical region within 11q24-qter for hypoplastic left heart and identification of a candidate gene, JAM3, expressed during cardiogenesis. Genomics, 79 (4), 475 - 478. (doi:10.1006/geno.2002.6742).

Record type: Article

Abstract

Hypoplastic left heart is a severe human congenital heart defect characterized by left ventricular hypoplasiawith aortic and mitral valve atresia. A genetic etiology is indicated by an association of the hypoplastic left heart phenotype with terminal 11q deletions that span approximately 20 Mb (distal to FRA11B in 11q23). Here we define the breakpoints in four patients with heart defects in association with distal 11q monosomy and refine the critical region to an approximately 9-Mb region distal to D11S1351. Within this critical region we have identified JAM3, a member of the junction adhesion molecule family, as a strong candidate gene for the cardiac phenotype on the basis that it is expressed during human cardiogenesis in the structures principally affected in hypoplastic left heart.

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Published date: 2002
Additional Information: Short communication

Identifiers

Local EPrints ID: 24902
URI: http://eprints.soton.ac.uk/id/eprint/24902
ISSN: 0888-7543
PURE UUID: 6312cc31-fb8c-4ba1-92c8-d263201d5007
ORCID for C. Spalluto: ORCID iD orcid.org/0000-0001-7273-0844

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Date deposited: 06 Apr 2006
Last modified: 16 Mar 2024 03:24

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Contributors

Author: H.M. Phillips
Author: G.L. Renforth
Author: C. Spalluto ORCID iD
Author: T. Hearn
Author: A.R. Curtis
Author: L. Craven
Author: B. Havarani
Author: M. Clement-Jones
Author: C. English
Author: O. Stumper
Author: T. Salmon
Author: S. Hutchinson
Author: M.S. Jackson
Author: D.I. Wilson

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