READ ME File For 'Dataset title' Dataset DOI: 10.5258/SOTON/D2354 Date that the file was created: August, 2022 ------------------- GENERAL INFORMATION ------------------- ReadMe Author: HELENA LEE, University of Southampton, ORCID ID 0000-0002-2573-9536 Date of data collection: February 2012 to July 2019 Information about geographic location of data collection: Leicester Royal Infirmary, UK Related projects: ADD IN -------------------------- SHARING/ACCESS INFORMATION -------------------------- Licenses/restrictions placed on the data, or limitations of reuse: Recommended citation for the data: Creative Commons Attribution CC-BY This dataset supports the publication: AUTHORS: Helena Lee, Ravi Purohit, Viral Sheth, Gail Maconachie, Zhanhan Tu, Mervyn G Thomas, Anastasia Pilat, Rebecca J McLean, Frank A Proudlock, and Irene Gottlob TITLE:Retinal development in infants and young children with albinism: evidence for plasticity in early childhood. JOURNAL:American Journal of Ophthalmology PAPER DOI:https://doi.org/10.1016/j.ajo.2022.08.028 Links to other publicly accessible locations of the data: None Links/relationships to ancillary or related data sets: None -------------------- DATA & FILE OVERVIEW -------------------- This dataset contains: 1. Albinism_Retinal_Development_Data This is an excel file containing all of the segmented optical coherence tomography retinal imaging measurements for each of the participants included in this study. Relationship between files, if important for context: N/A Additional related data collected that was not included in the current data package: N/A If data was derived from another source, list source: N/A If there are there multiple versions of the dataset, list the file updated, when and why update was made: N/A -------------------------- METHODOLOGICAL INFORMATION -------------------------- Description of methods used for collection/generation of data: Hand-held spectral domain optical coherence tomography (Leica Microsystems, Wetzlar, Germany) was used to obtain a 10 mm x 5 mm high-density volumetric scan (consisting of 100 B-scans and 500 A-scans per B-scan, with a distance of 50 µm between successive B-scans) of the foveal region as previously described (https://pubmed.ncbi.nlm.nih.gov/24222299/). The acquisition speed for each B scan was 5.8 ms with an overall scan time of 2.9 seconds, optical resolution of <4 μm and a digital resolution of 2.4 μm per pixel. Methods for processing the data: The acquired images were exported from the OCT software and imported into ImageJ software (available at: http:// rsbweb.nih.gov/ij/; Date accessed: May 11, 2012) where retinal layer segmentation was performed. The lateral scale of each image was estimated using previously reported pediatric axial length data (https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2868489/) which was also adjusted for refractive error based on information provided by the manufacturer. The nomenclature used to label the segmented layers are based on previously established anatomical correlates with histology (https://pubmed.ncbi.nlm.nih.gov/21844839/: https://pubmed.ncbi.nlm.nih.gov/12742848/). Software- or Instrument-specific information needed to interpret the data, including software and hardware version numbers: None Standards and calibration information, if appropriate: N/A Environmental/experimental conditions: All participants were imaged in the paediatric eye clinic at Leicester Royal Infirmary, using the Leica Microsystems hand-held optical coherence tomography system. Describe any quality-assurance procedures performed on the data: None People involved with sample collection, processing, analysis and/or submission: Helena Lee, Ravi Purohit, Viral Sheth, Gail Maconachie, Zhanhan Tu, Mervyn G Thomas, Anastasia Pilat, Rebecca J McLean, Frank A Proudlock, and Irene Gottlob -------------------------- DATA-SPECIFIC INFORMATION -------------------------- Number of variables: 1534 Number of cases/rows: 516 Variable list, defining any abbreviations, units of measure, codes or symbols used: agemonths, eye, race, agegroup, logmar, gender, diagnosis, rt2500n, rt2450n, rt2400n, rt2350n, rt2300n, rt2250n, rt2200n, rt2150n, rt2100n, rt2050n, rt2000n, rt1950n, rt1900n, rt1850n, rt1800n, rt1750n, rt1700n, rt1650n, rt1600n, rt1550n, rt1500n, rt1450n, rt1400n, rt1350n, rt1300n, rt1250n, rt1200n, rt1150n, rt1100n, rt1050n, rt1000n, rt950n, rt900n, rt850n, rt800n, rt750n, rt700n, rt650n, rt600n, rt550n, rt500n, rt450n, rt400n, rt350n, rt300n, rt250n, rt200n, rt150n, rt100n, rt50n, rt0, rt50t, rt100t, rt150t, rt200t, rt250t, rt300t, rt350t, rt400t, rt450t, rt500t, rt550t, rt600t, rt650t, rt700t, rt750t, rt800t, rt850t, rt900t, rt950t, rt1000t, rt1050t, rt1100t, rt1150t, rt1200t, rt1250t, rt1300t, rt1350t, rt1400t, rt1450t, rt1500t, rt1550t, rt1600t, rt1650t, rt1700t, rt1750t, rt1800t, rt1850t, rt1900t, rt1950t, rt2000t, rt2050t, rt2100t, rt2150t, rt2200t, rt2250t, rt2300t, rt2350t, rt2400t, rt2450t, rt2500t, fovealpitdepth, phtrls2500n, phtrls2450n, phtrls2400n, phtrls2350n, phtrls2300n, phtrls2250n, phtrls2200n, phtrls2150n, phtrls2100n, phtrls2050n, phtrls2000n, phtrls1950n, phtrls1900n, phtrls1850n, phtrls1800n, phtrls1750n, phtrls1700n, phtrls1650n, phtrls1600n, phtrls1550n, phtrls1500n, phtrls1450n, phtrls1400n, phtrls1350n, phtrls1300n, phtrls1250n, phtrls1200n, phtrls1150n, phtrls1100n, phtrls1050n, phtrls1000n, phtrls950n, phtrls900n, phtrls850n, phtrls800n, phtrls750n, phtrls700n, phtrls650n, phtrls600n, phtrls550n, phtrls500n, phtrls450n, phtrls400n, phtrls350n, phtrls300n, phtrls250n, phtrls200n, phtrls150n, phtrls100n, phtrls50n, phtrls0, phtrls50t, phtrls100t, phtrls150t, phtrls200t, phtrls250t, phtrls300t, phtrls350t, phtrls400t, phtrls450t, phtrls500t, phtrls550t, phtrls600t, phtrls650t, phtrls700t, phtrls750t, phtrls800t, phtrls850t, phtrls900t, phtrls950t, phtrls1000t, phtrls1050t, phtrls1100t, phtrls1150t, phtrls1200t, phtrls1250t, phtrls1300t, phtrls1350t, phtrls1400t, phtrls1450t, phtrls1500t, phtrls1550t, phtrls1600t, phtrls1650t, phtrls1700t, phtrls1750t, phtrls1800t, phtrls1850t, phtrls1900t, phtrls1950t, phtrls2000t, phtrls2050t, phtrls2100t, phtrls2150t, phtrls2200t, phtrls2250t, phtrls2300t, phtrls2350t, phtrls2400t, phtrls2450t, phtrls2500t, procls2500n, procls2450n, procls2400n, procls2350n, procls2300n, procls2250n, procls2200n, procls2150n, procls2100n, procls2050n, procls2000n, procls1950n, procls1900n, procls1850n, procls1800n, procls1750n, procls1700n, procls1650n, procls1600n, procls1550n, procls1500n, procls1450n, procls1400n, procls1350n, procls1300n, procls1250n, procls1200n, procls1150n, procls1100n, procls1050n, procls1000n, procls950n, procls900n, procls850n, procls800n, procls750n, procls700n, procls650n, procls600n, procls550n, procls500n, procls450n, procls400n, procls350n, procls300n, procls250n, procls200n, procls150n, procls100n, procls50n, procls0, procls50t, procls100t, procls150t, procls200t, procls250t, procls300t, procls350t, procls400t, procls450t, procls500t, procls550t, procls600t, procls650t, procls700t, procls750t, procls800t, procls850t, procls900t, procls950t, procls1000t, procls1050t, procls1100t, procls1150t, procls1200t, procls1250t, procls1300t, procls1350t, procls1400t, procls1450t, procls1500t, procls1550t, procls1600t, procls1650t, procls1700t, procls1750t, procls1800t, procls1850t, procls1900t, procls1950t, procls2000t, procls2050t, procls2100t, procls2150t, procls2200t, procls2250t, procls2300t, procls2350t, procls2400t, procls2450t, procls2500t, rpe2500n, rpe2450n, rpe2400n, rpe2350n, rpe2300n, rpe2250n, rpe2200n, rpe2150n, rpe2100n, rpe2050n, rpe2000n, rpe1950n, rpe1900n, rpe1850n, rpe1800n, rpe1750n, rpe1700n, rpe1650n, rpe1600n, rpe1550n, rpe1500n, rpe1450n, rpe1400n, rpe1350n, rpe1300n, rpe1250n, rpe1200n, rpe1150n, rpe1100n, rpe1050n, rpe1000n, rpe950n, rpe900n, rpe850n, rpe800n, rpe750n, rpe700n, rpe650n, rpe600n, rpe550n, rpe500n, rpe450n, rpe400n, rpe350n, rpe300n, rpe250n, rpe200n, rpe150n, rpe100n, rpe50n, rpe0, rpe50t, rpe100t, rpe150t, rpe200t, rpe250t, rpe300t, rpe350t, rpe400t, rpe450t, rpe500t, rpe550t, rpe600t, rpe650t, rpe700t, rpe750t, rpe800t, rpe850t, rpe900t, rpe950t, rpe1000t, rpe1050t, rpe1100t, rpe1150t, rpe1200t, rpe1250t, rpe1300t, rpe1350t, rpe1400t, rpe1450t, rpe1500t, rpe1550t, rpe1600t, rpe1650t, rpe1700t, rpe1750t, rpe1800t, rpe1850t, rpe1900t, rpe1950t, rpe2000t, rpe2050t, rpe2100t, rpe2150t, rpe2200t, rpe2250t, rpe2300t, rpe2350t, rpe2400t, rpe2450t, rpe2500t, osrpe2500n, osrpe2450n, osrpe2400n, osrpe2350n, osrpe2300n, osrpe2250n, osrpe2200n, osrpe2150n, osrpe2100n, osrpe2050n, osrpe2000n, osrpe1950n, osrpe1900n, osrpe1850n, osrpe1800n, osrpe1750n, osrpe1700n, osrpe1650n, osrpe1600n, osrpe1550n, osrpe1500n, osrpe1450n, osrpe1400n, osrpe1350n, osrpe1300n, osrpe1250n, osrpe1200n, osrpe1150n, osrpe1100n, osrpe1050n, osrpe1000n, osrpe950n, osrpe900n, osrpe850n, osrpe800n, osrpe750n, osrpe700n, osrpe650n, osrpe600n, osrpe550n, osrpe500n, osrpe450n, osrpe400n, osrpe350n, osrpe300n, osrpe250n, osrpe200n, osrpe150n, osrpe100n, osrpe50n, osrpe0, osrpe50t, osrpe100t, osrpe150t, osrpe200t, osrpe250t, osrpe300t, osrpe350t, osrpe400t, osrpe450t, osrpe500t, osrpe550t, osrpe600t, osrpe650t, osrpe700t, osrpe750t, osrpe800t, osrpe850t, osrpe900t, osrpe950t, osrpe1000t, osrpe1050t, osrpe1100t, osrpe1150t, osrpe1200t, osrpe1250t, osrpe1300t, osrpe1350t, osrpe1400t, osrpe1450t, osrpe1500t, osrpe1550t, osrpe1600t, osrpe1650t, osrpe1700t, osrpe1750t, osrpe1800t, osrpe1850t, osrpe1900t, osrpe1950t, osrpe2000t, osrpe2050t, osrpe2100t, osrpe2150t, osrpe2200t, osrpe2250t, osrpe2300t, osrpe2350t, osrpe2400t, osrpe2450t, osrpe2500t, rnfl2500n, rnfl2450n, rnfl2400n, rnfl2350n, rnfl2300n, rnfl2250n, rnfl2200n, rnfl2150n, rnfl2100n, rnfl2050n, rnfl2000n, rnfl1950n, rnfl1900n, rnfl1850n, rnfl1800n, rnfl1750n, rnfl1700n, rnfl1650n, rnfl1600n, rnfl1550n, rnfl1500n, rnfl1450n, rnfl1400n, rnfl1350n, rnfl1300n, rnfl1250n, rnfl1200n, rnfl1150n, rnfl1100n, rnfl1050n, rnfl1000n, rnfl950n, rnfl900n, rnfl850n, rnfl800n, rnfl750n, rnfl700n, rnfl650n, rnfl600n, rnfl550n, rnfl500n, rnfl450n, rnfl400n, rnfl350n, rnfl300n, rnfl250n, rnfl200n, rnfl150n, rnfl100n, rnfl50n, rnfl0, rnfl50t, rnfl100t, rnfl150t, rnfl200t, rnfl250t, rnfl300t, rnfl350t, rnfl400t, rnfl450t, rnfl500t, rnfl550t, rnfl600t, rnfl650t, rnfl700t, rnfl750t, rnfl800t, rnfl850t, rnfl900t, rnfl950t, rnfl1000t, rnfl1050t, rnfl1100t, rnfl1150t, rnfl1200t, rnfl1250t, rnfl1300t, rnfl1350t, rnfl1400t, rnfl1450t, 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onl1100t, onl1150t, onl1200t, onl1250t, onl1300t, onl1350t, onl1400t, onl1450t, onl1500t, onl1550t, onl1600t, onl1650t, onl1700t, onl1750t, onl1800t, onl1850t, onl1900t, onl1950t, onl2000t, onl2050t, onl2100t, onl2150t, onl2200t, onl2250t, onl2300t, onl2350t, onl2400t, onl2450t, onl2500t, onlis2500n, onlis2450n, onlis2400n, onlis2350n, onlis2300n, onlis2250n, onlis2200n, onlis2150n, onlis2100n, onlis2050n, onlis2000n, onlis1950n, onlis1900n, onlis1850n, onlis1800n, onlis1750n, onlis1700n, onlis1650n, onlis1600n, onlis1550n, onlis1500n, onlis1450n, onlis1400n, onlis1350n, onlis1300n, onlis1250n, onlis1200n, onlis1150n, onlis1100n, onlis1050n, onlis1000n, onlis950n, onlis900n, onlis850n, onlis800n, onlis750n, onlis700n, onlis650n, onlis600n, onlis550n, onlis500n, onlis450n, onlis400n, onlis350n, onlis300n, onlis250n, onlis200n, onlis150n, onlis100n, onlis50n, onlis0, onlis50t, onlis100t, onlis150t, onlis200t, onlis250t, onlis300t, onlis350t, onlis400t, onlis450t, onlis500t, onlis550t, onlis600t, onlis650t, onlis700t, onlis750t, onlis800t, onlis850t, onlis900t, onlis950t, onlis1000t, onlis1050t, onlis1100t, onlis1150t, onlis1200t, onlis1250t, onlis1300t, onlis1350t, onlis1400t, onlis1450t, onlis1500t, onlis1550t, onlis1600t, onlis1650t, onlis1700t, onlis1750t, onlis1800t, onlis1850t, onlis1900t, onlis1950t, onlis2000t, onlis2050t, onlis2100t, onlis2150t, onlis2200t, onlis2250t, onlis2300t, onlis2350t,,onlis2400t, onlis2450t, onlis2500t, is2500n, is2450n, is2400n, is2350n, is2300n, is2250n, is2200n, is2150n, is2100n, is2050n, is2000n, is1950n, is1900n, is1850n, is1800n, is1750n, is1700n, is1650n, is1600n, is1550n, is1500n, is1450n, is1400n, is1350n, is1300n, is1250n, is1200n, is1150n, is1100n, is1050n, is1000n, is950n, is900n, is850n, is800n, is750n, is700n, is650n, is600n, is550n, is500n, is450n, is400n, is350n, is300n, is250n, is200n, is150n, is100n, is50n, is0, is50t, is100t, is150t, is200t, is250t, is300t, is350t, is400t, is450t, is500t, is550t, is600t, is650t, is700t, is750t, is800t, is850t, is900t, is950t, is1000t, is1050t, is1100t, is1150t, is1200t, is1250t, is1300t, is1350t, is1400t, is1450t, is1500t, is1550t, is1600t, is1650t, is1700t, is1750t, is1800t, is1850t, is1900t, is1950t, is2000t, is2050t, is2100t, is2150t, is2200t, is2250t, is2300t, is2350t, is2400t, is2450t, is2500t, gcl2500n, gcl2450n, gcl2400n, gcl2350n, gcl2300n, gcl2250n, gcl2200n, gcl2150n, gcl2100n, gcl2050n, gcl2000n, gcl1950n, gcl1900n, gcl1850n, gcl1800n, gcl1750n, gcl1700n, gcl1650n, gcl1600n, gcl1550n, gcl1500n, gcl1450n, gcl1400n, gcl1350n, gcl1300n, gcl1250n, gcl1200n, gcl1150n, gcl1100n, gcl1050n, gcl1000n, gcl950n, gcl900n, gcl850n, gcl800n, gcl750n, gcl700n, gcl650n, gcl600n, gcl550n, gcl500n, gcl450n, gcl400n, gcl350n, gcl300n, gcl250n, gcl200n, gcl150n, gcl100n, gcl50n, gcl0, gcl50t, gcl100t, gcl150t, gcl200t, gcl250t, gcl300t, gcl350t, gcl400t, gcl450t, gcl500t, gcl550t, gcl600t, cl650t, gcl700t, gcl750t, gcl800t, gcl850t, gcl900t, gcl950t, gcl1000t, gcl1050t, gcl1100t, gcl1150t, gcl1200t, gcl1250t, gcl1300t, gcl1350t, gcl1400t, gcl1450t, gcl1500t, gcl1550t, gcl1600t, gcl1650t, gcl1700t, gcl1750t, gcl1800t, gcl1850t, gcl1900t, gcl1950t, gcl2000t, gcl2050t, gcl2100t, gcl2150t, gcl2200t, gcl2250t, gcl2300t, gcl2350t, gcl2400t, gcl2450t, gcl2500t, ipl2500n, ipl2450n, ipl2400n, ipl2350n, ipl2300n, ipl2250n, ipl2200n, ipl2150n, ipl2100n, ipl2050n, ipl2000n, ipl1950n, ipl1900n, ipl1850n, ipl1800n, ipl1750n, ipl1700n, ipl1650n, ipl1600n, ipl1550n, ipl1500n, ipl1450n, ipl1400n, ipl1350n, ipl1300n, ipl1250n, ipl1200n, ipl1150n, ipl1100n, ipl1050n, ipl1000n, ipl950n, ipl900n, ipl850n, ipl800n, ipl750n, ipl700n, ipl650n, ipl600n, ipl550n, ipl500n, ipl450n, ipl400n, ipl350n, ipl300n, ipl250n, ipl200n, ipl150n, ipl100n, ipl50n, ipl0, ipl50t, ipl100t, ipl150t, ipl200t, ipl250t, ipl300t, ipl350t, ipl400t, ipl450t, ipl500t, ipl550t, ipl600t, ipl650t, ipl700t, ipl750t, ipl800t, ipl850t, ipl900t, ipl950t, ipl1000t, ipl1050t, ipl1100t, ipl1150t, ipl1200t, ipl1250t, ipl1300t, ipl1350t, ipl1400t, ipl1450t, ipl1500t, ipl1550t, ipl1600t, ipl1650t, ipl1700t, ipl1750t, ipl1800t, ipl1850t, ipl1900t, ipl1950t, ipl2000t, ipl2050t, ipl2100t, ipl2150t, ipl2200t, ipl2250t, ipl2300t, ipl2350t, ipl2400t, ipl2450t, ipl2500t, inl2500n,inl2450n, inl2400n, inl2350n, inl2300n, inl2250n, inl2200n, inl2150n, inl2100n, inl2050n, inl2000n, inl1950n, inl1900n, inl1850n, inl1800n, inl1750n, inl1700n, inl1650n, inl1600n, inl1550n, inl1500n, inl1450n, inl1400n, inl1350n, inl1300n, inl1250n, inl1200n, inl1150n, inl1100n, inl1050n, inl1000n, inl950n, inl900n, inl850n, inl800n, inl750n, inl700n, inl650n, inl600n, inl550n, inl500n, inl450n, inl400n, inl350n, inl300n, inl250n, inl200n, inl150n, inl100n, inl50n, inl0, inl50t, inl100t, inl150t, inl200t, inl250t, inl300t, inl350t, inl400t, inl450t, inl500t, inl550t, inl600t, inl650t, inl700t, inl750t, inl800t, inl850t, inl900t, inl950t, inl1000t, inl1050t, inl1100t, inl1150t, inl1200t, inl1250t, inl1300t, inl1350t, inl1400t, inl1450t, inl1500t, inl1550t, inl1600t, inl1650t, inl1700t, inl1750t, inl1800t, inl1850t, inl1900t, inl1950t, inl2000t, inl2050t, inl2100t, inl2150t, inl2200t, inl2250t, inl2300t, inl2350t, inl2400t, inl2450t, inl2500t, cost2500n, cost2450n, cost2400n, cost2350n, cost2300n, cost2250n, cost2200n, cost2150n, cost2100n, cost2050n, cost2000n, cost1950n, cost1900n, cost1850n, cost1800n, cost1750n, cost1700n, cost1650n, cost1600n, cost1550n, cost1500n, cost1450n, cost1400n, cost1350n, cost1300n, cost1250n, cost1200n, cost1150n, cost1100n, cost1050n, cost1000n, cost950n, cost900n, cost850n, cost800n, cost750n, cost700n, cost650n, cost600n, cost550n, cost500n, cost450n, cost400n, cost350n, cost300n, cost250n, cost200n, cost150n, cost100n, cost50n, cost0, cost50t, cost100t, cost150t, cost200t, cost250t, cost300t, cost350t, cost400t, cost450t, cost500t, cost550t, cost600t, cost650t, cost700t, cost750t, cost800t, cost850t, cost900t, cost950t, cost1000t, cost1050t, cost1100t, cost1150t, cost1200t, cost1250t, cost1300t, cost1350t, cost1400t, cost1450t, cost1500t, cost1550t, cost1600t, cost1650t, cost1700t, cost1750t, cost1800t, cost1850t, cost1900t, cost1950t, cost2000t, cost2050t, cost2100t, cost2150t, cost2200t, cost2250t, cost2300t, cost2350t, cost2400t, cost2450t, cost2500t Codes & Abbreviations Eye OD 1 OS 2 Race Caucasian 1 Asian 2 Afro-Caribbean 3 Other 4 Age Categories