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A longitudinal study of the 5xFAD mouse retina delineates Amyloid beta (Ab)-mediated retinal pathology from age-related changes

A longitudinal study of the 5xFAD mouse retina delineates Amyloid beta (Ab)-mediated retinal pathology from age-related changes
A longitudinal study of the 5xFAD mouse retina delineates Amyloid beta (Ab)-mediated retinal pathology from age-related changes
Background: age-related macular degeneration (AMD) is the commonest cause of irreversible blindness in developed societies. AMD coincides with advanced age to which genetic and lifestyle factors contribute additional risks. High levels of the Alzheimer’s-linked Amyloid beta (Ab) proteins are correlated with aged/AMD retinas. To delineate the role of Ab in retinopathy from age-related changes, we used transgenic 5xFAD mice in a longitudinal study to recapitulate the aged/AMD Ab-burden of the human retina.

Methods: mice were genotyped to exclude the retinal degeneration alleles Pde6brd1, Pde6brd8, Agouti, Tyr and Oca2. Retinas of 5xFAD and wildtype littermates (97 males/females in total) were longitudinally assessed until 15 months using non-invasive retinal scans: multi-focal electroretinography, optokinetic tracking, optical coherence tomography (OCT), colour fundus photography and fluorescein angiography. Mice were killed at 4, 8 and 15 months, and eyes enucleated for analyses by light, confocal and electron microscopy.

Results: age-related changes included a gradual decline of retinal activity in all mice. Subretinal/drusen-like deposits increased with age, but, like retinal vessel morphology and vessel integrity, showed no differences between cohorts. Diminished PSD95 levels indicated impaired photoreceptor-bipolar connectivity which correlated with age. Ultrastructural imaging showed increased electron-dense granules and undigested outer segments within retinal pigment epithelial cells with age. 5xFAD pathology included significant weight reduction vs. wildtype/littermates, which were pronounced in females. 8 month old 5xFAD mice had diminished A and B waves, though the age-related decline in wildtype mice abolished these subsequently. Visual acuity/function was also reduced in 14 month 5xFAD eyes. OCT revealed thickened photoreceptor nuclei and inner segments in 8 month 5xFAD retinae. Scrutiny of chorioretinal tissues revealed diminished photoreceptor nuclei in 4 month 5xFAD eyes, though differences were abolished as both cohorts aged. From 8 months onwards, 5xFAD mice possessed fewer bipolar cell nuclei.

Conclusions: chronic Ab exposure led to the earlier development of retinopathy-linked features, the identification of which advances our understanding of how Ab contributes to multifaceted retinopathies. These were distinguishable from wider age-related changes and non-specific influences of retinal degeneration alleles in 5xFAD mice. Longitudinal analyses revealed sex and age-related limitations and important 3Rs considerations for future studies using 5xFAD mice.
5xFAD, Age, Age-related Macular Degeneration (AMD), Amyloid beta (Aβ), Mouse model, Retina, Retinopathy
1758-9193
Lynn, Savannah A.
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Pandi, Sudha Priya Soundara
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Sanchez‑Bretano, Aida
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Muir, Anna Marie
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Parker, Lidia
ac630b90-5743-48b8-8862-b0258c420ac7
Chatelet, David S.
074550ec-3a37-4a8a-8ae6-68e085af69cd
Newall, Tutte
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Scott, Jennifer A.
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Keeling, Eloise
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Smyth, Neil R.
0eba2a40-3b43-4d40-bb64-621bd7e9d505
Self, Jay E.
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Lotery, Andrew J.
5ecc2d2d-d0b4-468f-ad2c-df7156f8e514
Lee, Helena
5d36fd1e-9334-4db5-b201-034d147133fb
Ratnayaka, J. Arjuna
002499b8-1a9f-45b6-9539-5ac145799dfd
Lynn, Savannah A.
177ed471-999b-4420-b6f6-d24a85b72524
Pandi, Sudha Priya Soundara
793aefcd-f751-44ea-bd38-dd150f1062b6
Sanchez‑Bretano, Aida
a6855823-638f-4041-94d3-6299525e8e20
Muir, Anna Marie
3bb9296c-28a5-4c92-94c6-81d68115276a
Parker, Lidia
ac630b90-5743-48b8-8862-b0258c420ac7
Chatelet, David S.
074550ec-3a37-4a8a-8ae6-68e085af69cd
Newall, Tutte
2ed01da6-a355-4849-b5b9-aa862903c95b
Scott, Jennifer A.
72761f3a-6e75-4057-a947-ae2f02ca2612
Keeling, Eloise
3207bbdb-d391-44af-8abc-a60c08dce45b
Smyth, Neil R.
0eba2a40-3b43-4d40-bb64-621bd7e9d505
Self, Jay E.
0f6efc58-ae24-4667-b8d6-6fafa849e389
Lotery, Andrew J.
5ecc2d2d-d0b4-468f-ad2c-df7156f8e514
Lee, Helena
5d36fd1e-9334-4db5-b201-034d147133fb
Ratnayaka, J. Arjuna
002499b8-1a9f-45b6-9539-5ac145799dfd

Lynn, Savannah A., Pandi, Sudha Priya Soundara, Sanchez‑Bretano, Aida, Muir, Anna Marie, Parker, Lidia, Chatelet, David S., Newall, Tutte, Scott, Jennifer A., Keeling, Eloise, Smyth, Neil R., Self, Jay E., Lotery, Andrew J., Lee, Helena and Ratnayaka, J. Arjuna (2025) A longitudinal study of the 5xFAD mouse retina delineates Amyloid beta (Ab)-mediated retinal pathology from age-related changes. Alzheimer's Research & Therapy, 17 (1), [136]. (doi:10.1186/s13195-025-01784-w).

Record type: Article

Abstract

Background: age-related macular degeneration (AMD) is the commonest cause of irreversible blindness in developed societies. AMD coincides with advanced age to which genetic and lifestyle factors contribute additional risks. High levels of the Alzheimer’s-linked Amyloid beta (Ab) proteins are correlated with aged/AMD retinas. To delineate the role of Ab in retinopathy from age-related changes, we used transgenic 5xFAD mice in a longitudinal study to recapitulate the aged/AMD Ab-burden of the human retina.

Methods: mice were genotyped to exclude the retinal degeneration alleles Pde6brd1, Pde6brd8, Agouti, Tyr and Oca2. Retinas of 5xFAD and wildtype littermates (97 males/females in total) were longitudinally assessed until 15 months using non-invasive retinal scans: multi-focal electroretinography, optokinetic tracking, optical coherence tomography (OCT), colour fundus photography and fluorescein angiography. Mice were killed at 4, 8 and 15 months, and eyes enucleated for analyses by light, confocal and electron microscopy.

Results: age-related changes included a gradual decline of retinal activity in all mice. Subretinal/drusen-like deposits increased with age, but, like retinal vessel morphology and vessel integrity, showed no differences between cohorts. Diminished PSD95 levels indicated impaired photoreceptor-bipolar connectivity which correlated with age. Ultrastructural imaging showed increased electron-dense granules and undigested outer segments within retinal pigment epithelial cells with age. 5xFAD pathology included significant weight reduction vs. wildtype/littermates, which were pronounced in females. 8 month old 5xFAD mice had diminished A and B waves, though the age-related decline in wildtype mice abolished these subsequently. Visual acuity/function was also reduced in 14 month 5xFAD eyes. OCT revealed thickened photoreceptor nuclei and inner segments in 8 month 5xFAD retinae. Scrutiny of chorioretinal tissues revealed diminished photoreceptor nuclei in 4 month 5xFAD eyes, though differences were abolished as both cohorts aged. From 8 months onwards, 5xFAD mice possessed fewer bipolar cell nuclei.

Conclusions: chronic Ab exposure led to the earlier development of retinopathy-linked features, the identification of which advances our understanding of how Ab contributes to multifaceted retinopathies. These were distinguishable from wider age-related changes and non-specific influences of retinal degeneration alleles in 5xFAD mice. Longitudinal analyses revealed sex and age-related limitations and important 3Rs considerations for future studies using 5xFAD mice.

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Accepted/In Press date: 5 June 2025
Published date: 19 June 2025
Keywords: 5xFAD, Age, Age-related Macular Degeneration (AMD), Amyloid beta (Aβ), Mouse model, Retina, Retinopathy

Identifiers

Local EPrints ID: 503493
URI: http://eprints.soton.ac.uk/id/eprint/503493
ISSN: 1758-9193
PURE UUID: a6fd16e5-9591-4b8b-84ad-8490235f3f50
ORCID for Savannah A. Lynn: ORCID iD orcid.org/0000-0003-2513-3144
ORCID for Eloise Keeling: ORCID iD orcid.org/0000-0003-0399-359X
ORCID for Jay E. Self: ORCID iD orcid.org/0000-0002-1030-9963
ORCID for Andrew J. Lotery: ORCID iD orcid.org/0000-0001-5541-4305
ORCID for Helena Lee: ORCID iD orcid.org/0000-0002-2573-9536
ORCID for J. Arjuna Ratnayaka: ORCID iD orcid.org/0000-0002-1027-6938

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Date deposited: 04 Aug 2025 16:45
Last modified: 22 Aug 2025 02:27

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Contributors

Author: Savannah A. Lynn ORCID iD
Author: Sudha Priya Soundara Pandi
Author: Aida Sanchez‑Bretano
Author: Anna Marie Muir
Author: Lidia Parker
Author: David S. Chatelet
Author: Tutte Newall
Author: Jennifer A. Scott
Author: Eloise Keeling ORCID iD
Author: Neil R. Smyth
Author: Jay E. Self ORCID iD
Author: Helena Lee ORCID iD

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