Vision loss due to coincident ocular and central causes in a patient with Heidenhain variant Creutzfeldt-Jakob disease
Vision loss due to coincident ocular and central causes in a patient with Heidenhain variant Creutzfeldt-Jakob disease
Creutzfeldt-Jakob disease (CJD) is a degenerative disease of the brain associated with a rapidly progressive spongiform encephalopathy. Visual symptoms and neuro-ophthalmological signs are not infrequent, and presentation to an ophthalmologist may result. A case is reported of an 89-years-old gentleman who presented with a short history of isolated deterioration in vision. He underwent ocular intervention but subsequently developed progressive dementia, asterixis, myoclonus, cerebellar and extrapyramidal signs, and cortical blindness. An electroencephalogram was consistent with CJD. The patient progressively deteriorated and died 9 weeks after symptom onset. Limited post-mortem examination confirmed CJD
creutzfeldt-jakob-disease, cortical blindness, myoclonus, creutzfeldt-jakob disease, dementia, disease, symptoms, elderly
231-232
Foundas, M.
5739fd62-14e1-4bce-a26d-bcb71a619740
Donaldson, M.D.
1a09fadc-4f88-4384-970d-ff75f84176f4
McAllister, I.L.
c963c229-05f5-44fc-bc5f-3459edb57b80
Bridges, L.R.
4858d61d-57ff-4265-9164-745dc342ca4c
2008
Foundas, M.
5739fd62-14e1-4bce-a26d-bcb71a619740
Donaldson, M.D.
1a09fadc-4f88-4384-970d-ff75f84176f4
McAllister, I.L.
c963c229-05f5-44fc-bc5f-3459edb57b80
Bridges, L.R.
4858d61d-57ff-4265-9164-745dc342ca4c
Foundas, M., Donaldson, M.D., McAllister, I.L. and Bridges, L.R.
(2008)
Vision loss due to coincident ocular and central causes in a patient with Heidenhain variant Creutzfeldt-Jakob disease.
Age and Ageing, 37 (2), .
(doi:10.1093/ageing/Afm19).
Abstract
Creutzfeldt-Jakob disease (CJD) is a degenerative disease of the brain associated with a rapidly progressive spongiform encephalopathy. Visual symptoms and neuro-ophthalmological signs are not infrequent, and presentation to an ophthalmologist may result. A case is reported of an 89-years-old gentleman who presented with a short history of isolated deterioration in vision. He underwent ocular intervention but subsequently developed progressive dementia, asterixis, myoclonus, cerebellar and extrapyramidal signs, and cortical blindness. An electroencephalogram was consistent with CJD. The patient progressively deteriorated and died 9 weeks after symptom onset. Limited post-mortem examination confirmed CJD
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Published date: 2008
Keywords:
creutzfeldt-jakob-disease, cortical blindness, myoclonus, creutzfeldt-jakob disease, dementia, disease, symptoms, elderly
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Local EPrints ID: 62372
URI: http://eprints.soton.ac.uk/id/eprint/62372
ISSN: 0002-0729
PURE UUID: f6a3aa56-4eb0-44b7-838c-c73f15deaa58
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Date deposited: 02 Sep 2008
Last modified: 15 Mar 2024 11:30
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Contributors
Author:
M. Foundas
Author:
M.D. Donaldson
Author:
I.L. McAllister
Author:
L.R. Bridges
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